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Chapter 21 - Epilepsy Syndromes

from Part III - Specific Conditions

Published online by Cambridge University Press:  24 June 2021

Neville M. Jadeja
Neville M. Jadeja
Affiliation:
University of Massachusetts Medical School
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Summary

Epilepsy syndromes (electroclinical syndromes) are well-recognized groupings of clinical (seizure types) and EEG features that occur together. Each syndrome typically shares a common age of onset, deficits (intellectual dysfunction), treatment, and prognosis. Syndromes are classified based on their onset, epilepsy type (focal, generalized, or mixed), and development of epileptic encephalopathy (disorder in which epileptic activity contributes to severe impairments in cognition and behavior). Relatively benign syndromes are typically associated with focal, generalized tonic clonic (GTC), typical absences, and myoclonic seizures. Epileptic encephalopathies are typically associated with atonic, tonic, atypical absences, and epileptic spasms in addition to the preceding seizure types.

Keywords

epilepsy sydromesneonatalinfantilechildhoodadolescentadulthoodless age specific
Type
Chapter
Information
How to Read an EEG , pp. 195 - 213
Publisher: Cambridge University Press
Print publication year: 2021

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